Zitieren

Background

Polycythemia vera has been found in a wide range of hematopoietic tissue disorders, but rarely concomitant with renal abnormality. To our knowledge there is only one available report of a patient with polycythemia vera concomitant with renal angiomyolipoma, and the report does not cover the clinical course of this rare finding.

Objectives

To report the presentation and clinical course of a patient with polycythemia vera concomitant with right renal angiomyolipoma.

Methods

We retrospectively reviewed the medical records of a patient with polycythemia vera who presented with renal angiomyolipoma.

Results

Our patient presented with a right renal mass and polycythemia vera diagnosed by a point mutation in the gene for Janus kinase 2. The mass was diagnosed as renal angiomyolipoma on histopathology. After partial nephrectomy, she was prescribed a low dosage of hydroxyurea without the return of erythrocytosis for a year.

Conclusions

Polycythemia vera responded well to low dosage hydroxyurea, which controlled erythrocytosis after removing the renal mass.

eISSN:
1875-855X
Sprache:
Englisch
Zeitrahmen der Veröffentlichung:
6 Hefte pro Jahr
Fachgebiete der Zeitschrift:
Medizin, Gesundheitsfachberufe, Vorklinische Medizin, Grundlagenmedizin, andere, Klinische Medizin