Fahr’s Syndrome and Secondary Hypoparathyroidism

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A typical case of Fahr’s syndrome is described in a 76-year-old Brazilian female who underwent a total thyroidectomy three decades ago. Six years before the current admission, she started with generalized tonic-clonic seizures. Associated disorders involved extra-pyramidal, cognitive, nocturnal terror and mood changes. With suspicion of hypocalcemia due to secondary hypoparathyroidism, laboratory determinations confirmed the diagnoses. Furthermore, imaging studies of the central nervous system detected multiple calcifications, with characteristic distribution of Fahr’s syndrome. Clinical management was successful.

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  • 1. BRONCEL M KORIZOG M ZABIELSKA J POLIWCZAK AR. Recurrent syncope and hypocalcaemic cardiomyopathy as manifestations of Fahr’s syndrome. Arch Med Sci 2010; 6:117-121.

  • 2. GÜLSÜN M BAYKIZ AF KABATAŞ S BELLI H. Fahr syndrome. Three cases presenting with psychiatric signs. Eur J Gen Med 2006; 3:35-40.

  • 3. SAVA A DUMITRESCU G HABA D HODOROG D MIHAILOV C SAPTE E. The Fahr syndrome and the chronic lymphocytic thyroiditis. Rom J Morphol Embryol 2013; 54:195-200.

  • 4. VEGA MG SOUSA AA LUCCA JR F PURICH S TENASSI ML. [Extrapyramidal syndrome and hypoparathyroidism. On the identity of Fahr disease]. Arq Neuropsiquiatr 1994; 52:419-426.

  • 5. KHAN MI WAGUENSPACK SG HU MI. Medical management of postsurgical hypoparathyroidism. Endocr Pract 2011; 17:18-25.

  • 6. KÜMMER A CASTRO M CARAMELLI P CARDOSO F TEIXEIRA AL. [Severe behavioral changes in a patient with Fahr's disease]. Arq Neuropsiquiatr 2006; 64:645-649.

  • 7. GULCELIK MA KURU B DINCER H et al. Complications of completion versus total thyroidectomy. Asian Pac J Cancer Prev 2012; 13:5225-5228.

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