Right Atrial Thrombosis in the Fetus with Dilatation of the Right Atrium with in Utero Spontaneous Resolution - A Case Report with Neonatal Follow-Up

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Abstract

We present an extraordinary case of congenital enlargement of the right atrium diagnosed at 31 weeks of gestation. This case emphasizes the fact that timing of the detection of this particular cardiac malformation is of capital importance to tract the optimal treatment strategy in order to monitor further progression (in this case accompanying thrombosis) and prevent complications.

1. Forbes K, Kantoch MJ, Divekar A, Ross D and Rebeyka IM. Management of infants with idiopathic dilatation of the right atrium and atrial tachycardia. Pediatric Cardiology. 2007;28:289-96.

2. Hofmann SR, Heilmann A, Hausler HJ, Dahnert I, Kamin G and Lachmann R. Congenital idiopathic dilatation of the right atrium: antenatal appearance, postnatal management, long-term follow-up and possible pathomechanism. Fetal Diagnosis and Therapy. 2012;32:256-61.

3. Imren Y, Halit V, Kula S and Olgunturk R. Giant right atrial aneurysm: case report. International Journal of Cardiology. 2006;112:e66-8.

4. Binder TM, Rosenhek R, Frank H, Gwechenberger M, Maurer G and Baumgartner H. Congenital malformations of the right atrium and the coronary sinus: an analysis based on 103 cases reported in the literature and two additional cases. Chest. 2000;117:1740-8.

5. Pernot C, Hoeffel JC and Jacob F. Idiopathic dilatation of the right atrium revealed in childhood by dysrhythmias. Pediatric Radiology. 1977;6:52-4.

6. Marin-Garcia J and Allen RG. Idiopathic dilatation of the right atrium: postoperative followup in a child. Journal of Pediatric Surgery. 1983;18:196-8.

7. Bhupali AN, Patankar KB, Paranjpe FS and Tamhane AU. Giant right atrium in a foetus. Indian Heart J. 2013;65:493-5.

8. Wagner N, Kagan KO, Abele H, Hoopmann M, Kaulitz R and Hofbeck M. Fetal idiopathic dilatation of the right atrium. Ultraschall Med. 2011;32:81-2.

9. Enzensberger C, Kreymborg KG, Valeske K, Apitz C, Akinturk H, Schranz D and Axt-Fliedner R. Management of idiopathic giant dilatation of the right atrium with subsequent atrial tachycardia. Arch Gynecol Obstet. 2013;288:705-7.

10. Shah K and Walsh K. Giant right atrial diverticulum: an unusual cause of Wolff-Parkinson-White syndrome. Br Heart J. 1992;68:58-9.

11. Rutledge J, Robertson MA, Kantoch M and Dyck J. Idiopathic dilation of the right atrium: case report and survey of the literature. Can J Cardiol. 1997;13:855-7.

12. Silva AM, Witsemburg M, Elzenza N, Stewart P. Idiopathic dilatation of the right atrium diagnosed in utero. Rev Port Cardiol 1992; 11: 161-3.

13. Papagiannis J, Chatzis a, Sarris G. Giant right atrial aneurysm: a case report. Int J Cardiol. 2008;129:e5-e6. doi:10.1016/j.ijcard.2007.06.081.

14. Lee Y, Cho J, Kim G, Lee S, Hyun M, Kim Y. Surgical Repair of Giant Right Atrial Aneurysm in a Neonate. Korean Circ J. 2011;41:331. doi:10.4070/kcj.2011.41.6.331.

15. Walter C, Carretero JM, Bartrons J, et al. Idiopathic dilatation of the right atrium. Report of four fetal cases. Hospital Sant Joan de Déu. Barcelona. Spain. Abstract AEPC

16. Nagata H, Stambach D, Wilson GJ, Menon A, Jaeggi E. Fetal Diagnosis of Right Atrial Aneurysms. Can J Cardiol. 2015. doi:10.1016/j.cjca.2015.11.002.

17. Ferreira M, Barberato A, Barberato SH, Gomes CC, Costa SL, Krawiec A. Right Atrial Aneurysm Associated to Fetal Hydrops: Diagnosis through Fetal Echocardiography. Arquivos Brasileiros de Cardiologia 2005;85:2004-2005.

18. Reinhardt-Owlya L, Sekarski N, Hurni M, et al. [Idiopathic dilatation of the right atrium simulating Ebstein’s anomaly: apropos of a case diagnosed in utero]. Arch Mal Coeur Vaiss 1998;91:645-9.

19. Tejero-Hernandez MA, Espejo-Perez S, Suarez-de- Lezo-Cruz-Conde J. Congenital Aneurysm of the Right Atrial Appendage in a Newborn: a Rare Anomaly. Rev Espanola Cardiol (English Ed. 2012;65(1):99-100. doi:10.1016/j. rec.2011.03.028

20. Sumner RG, Phillips JH, Jacoby WJ, Jr. and Tucker DH. Idiopathic enlargement of the right atrium. Circulation. 1965;32:985-91.

21. Blondheim DS, Klein R, Plich M and Marmor AT. Familial idiopathic dilatation of the right atrium with complete atrio-ventricular block: a new syndrome? Cardiology. 2000;94:224-6.

22. Blaysat G, Villain E, Marcon F, Rey C, Lipka J, Lefevre M and Bourlon F. [Prognosis and outcome of idiopathic dilatation of the right atrium in children. A cooperative study of 15 cases]. Arch Mal Coeur Vaiss. 1997;90:645-8.

23. Greer I, Hunt BJ. Low molecular weight heparin in pregnancy: Current issues. Br J Haematol. 2005;128:593-601. doi:10.1111/j.1365-2141.2004.05304.x.

24. Sanson, B J et al. “Safety of low-molecular-weight heparin in pregnancy: a systematic review.” Thrombosis and haemostasis 81.5 (1999) : 668-72.

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