Treatment of patients with functional single-ventricle physiology is achieved using surgical corrections known as the “Fontan Procedure”. Two separate blood circulations are created from the single-ventricle function. These are non-cyanogenic patients, but at high risk of developing HF. CRT implantation is an option to improve the functional class and EF.
5. Krentzer G Galindez E An operation of the correction of tricuspid atresia – Torac cardiovascular surgery 1973; 66: 613-621.
6. Sistino JJ Bonilha HS. Improvements in survival and neurodevelopmental outcomes in surgical treatment of hypoplastic left heart syndrome: a meta-analytic review. J Extra Corpor Technol. 2012; 44 216-223.
7. Ota N Fujimoto Y Murata M et al. Impact of prospective hemodynamics in patients with functional single ventricle undergoing Fontan complications JACC 2012; 94 1370-1377.
8. Quinton E Nightingale P Hudsmith L et.al. Prevalence of atrial tachyarrhythmia in adults after Fontan operation. Heart 2015; 1011672-1677.