Clinical report. The Fontan procedure for patients with a single lung

Background: Single lung Fontan procedure has been performed in patients with a congenital heart disease and a single functional lung. The procedure has not been reported in China.

Objective and Methods: We reported on the case of a 6-year-old child who had a single functional right ventricle, and an atretic left pulmonary artery, who underwent a successful Fontan operation into the single right pulmonary artery. The literature of Fontan procedure in the presence of a single lung is reviewed.

Results: The patient to relate the procedure well and had uneventful recovery. The patient has been followed up for more than two years with reasonable hemodynamics.

Conclusion: The single lung Fontan operation is possible with good outcomes. More patients and longer follow up will be required to standardize the strategies and to document utility of this procedure.