Mesenteric fibromatosis with intestinal involvement mimicking a gastrointestinal stromal tumour

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Mesenteric fibromatosis with intestinal involvement mimicking a gastrointestinal stromal tumour

Introduction. Mesenteric fibromatosis or intra-abdominal desmoid tumour is a rare proliferative disease affecting the mesentery. It is a locally aggressive tumour that lacks metastatic potential, but the local recurrence is common. Mesenteric fibromatosis with the intestinal involvement can be easily confused with other primary gastrointestinal tumours, especially with that of the mesenchymal origin.

Case report. We report a case of a 44-year-old female who presented with an abdominal mass that radiologically and pathologically mimicked a gastrointestinal stromal tumour.

Conclusions. The diagnosis of mesenteric fibromatosis should always be considered in the case of mesenchymal tumours apparently originating from the bowel wall that diffusely infiltrate the mesentery.

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Radiology and Oncology

The Journal of Association of Radiology and Oncology

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